quarta-feira, 19 de junho de 2013

Von Gierke disease

Glycogenosis
lysosomal glucosidase
Pompe disease

Glycogenosis type III
amyl-1 ,6-glucosidase
Cori's disease or disease Forbes
Glycogenosis type IV
amyl-1 ,4-1 ,6-glucosidase
Andersen disease
Glycogenosis type V
muscle glycogen phosphorylase
McArdle's disease
Glycogenosis type VI
liver glycogen phosphorylase
Hers disease
Glycogenosis type VII
muscle phosphofructokinase
Tarui disease
Glycogenosis type IX
phosphorylase kinase
-
Glycogenosis type XI
glucose transporter
Fanconi-Bickel disease
Glycogen storage disease type 0

glycogen synthetase

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